Colony-forming unit assay
| Patient identification . | Age (y) . | CFU-GM . | CFU-E . | CFU-Mk 1* . | CFU-Mk 2† . |
|---|---|---|---|---|---|
| CAMT-1 | 0.3 | 93 | 51 | 0 | 15 |
| CAMT-6 | 0.8 | 52 | 26 | 0 | 4 |
| CAMT-7 | 1.4 | 149 | 29 | 2 | 15 |
| 5.6 | 2 | 1 | 0 | 0 | |
| CAMT-9 | 3.0 | 3 | 3 | 0 | 0 |
| CAMT-17 | 0.8 | 52 | 2 | 0 | 7 |
| Controls (mean ± SD, n = 5) | 168 ± 40 | 139 ± 66 | 42 ± 13 | 69 ± 23 |
| Patient identification . | Age (y) . | CFU-GM . | CFU-E . | CFU-Mk 1* . | CFU-Mk 2† . |
|---|---|---|---|---|---|
| CAMT-1 | 0.3 | 93 | 51 | 0 | 15 |
| CAMT-6 | 0.8 | 52 | 26 | 0 | 4 |
| CAMT-7 | 1.4 | 149 | 29 | 2 | 15 |
| 5.6 | 2 | 1 | 0 | 0 | |
| CAMT-9 | 3.0 | 3 | 3 | 0 | 0 |
| CAMT-17 | 0.8 | 52 | 2 | 0 | 7 |
| Controls (mean ± SD, n = 5) | 168 ± 40 | 139 ± 66 | 42 ± 13 | 69 ± 23 |
CFU-GM = colony-forming unit-granulocyte-macrophage; CFU-E = colony-forming unit-erythrocyte; CFU-Mk 1 = colony-forming unit-megakaryocyte 1; CFU-Mk 2 = CFU-Mk 2.
Colonies per 105 BM-MNCs; 1 with TPO alone; 2 with IL-3, IL-6, TPO.