Table 2. Sites of thrombosis in 29 out... | American Society of Hematology

Table 2.

Sites of thrombosis in 29 out of 163 cases of PNH

UPN	Site of thrombosis	Years after diagnosis	Granulocyte PNH clone size, %	Red cell PNH clone size, %^*
	Liver-related
5	Portal vein (probable cause of death)	5	Not known	64
6	Hepatic vein	4	99.4	33.4
8	Hepatic vein	0	97.96	30.88
10	Portal vein + sagittal sinus (pregnant)	15	Not known	52
17	Hepatic + portal veins	0	Not known	100
27	Portal vein	8	99.6	89.59
33	Hepatic vein, shunt thrombosis	14	97.8	64
40	Portal vein	5	97	57
53	`Liver' (cause of death)	4	78	23
80	Portal vein (cause of death)	0	98	15.1
95	Hepatic vein—2 events	0	80	22.99
98	Hepatic vein	Not known	68.1	67.66
104	Hepatic vein	Not known†	Not known†	Not known†
107	Hepatic vein (cause of death)	0	99.5	49.81
109	Portal vein	0	99.9	5.73
149	Hepatic vein	0	98.3	83.4
153	Portal vein, pulmonary embolus	0.25	96.3	67.8
165	Hepatic vein—2 events	2.25	98.9	21.1
	Other
3	Deep venous thrombosis—2 events	7	9.7	4.4
22	Pulmonary embolus (Factor V Leiden heterozygote)	2	90.82	20.9
26	Superficial thrombophlebitis	1	55	24
34	Deep venous thrombosis	5	73	45
48	Cerebral vein thrombosis	8.75	92.9	77.4
61	Line thrombosis	1	67.62	21
70	Retinal vein	4	76.04	11.66
119	Thrombosis right cerebellum (Factor V Leiden heterozygote)	0	15.3	7.21
144	Deep venous thrombosis	0	96.6	43.2
146	Pulmonary embolus	0.8	84	57.4
177	Pulmonary embolus	7	97.1	81.5

UPN	Site of thrombosis	Years after diagnosis	Granulocyte PNH clone size, %	Red cell PNH clone size, %^*
	Liver-related
5	Portal vein (probable cause of death)	5	Not known	64
6	Hepatic vein	4	99.4	33.4
8	Hepatic vein	0	97.96	30.88
10	Portal vein + sagittal sinus (pregnant)	15	Not known	52
17	Hepatic + portal veins	0	Not known	100
27	Portal vein	8	99.6	89.59
33	Hepatic vein, shunt thrombosis	14	97.8	64
40	Portal vein	5	97	57
53	`Liver' (cause of death)	4	78	23
80	Portal vein (cause of death)	0	98	15.1
95	Hepatic vein—2 events	0	80	22.99
98	Hepatic vein	Not known	68.1	67.66
104	Hepatic vein	Not known†	Not known†	Not known†
107	Hepatic vein (cause of death)	0	99.5	49.81
109	Portal vein	0	99.9	5.73
149	Hepatic vein	0	98.3	83.4
153	Portal vein, pulmonary embolus	0.25	96.3	67.8
165	Hepatic vein—2 events	2.25	98.9	21.1
	Other
3	Deep venous thrombosis—2 events	7	9.7	4.4
22	Pulmonary embolus (Factor V Leiden heterozygote)	2	90.82	20.9
26	Superficial thrombophlebitis	1	55	24
34	Deep venous thrombosis	5	73	45
48	Cerebral vein thrombosis	8.75	92.9	77.4
61	Line thrombosis	1	67.62	21
70	Retinal vein	4	76.04	11.66
119	Thrombosis right cerebellum (Factor V Leiden heterozygote)	0	15.3	7.21
144	Deep venous thrombosis	0	96.6	43.2
146	Pulmonary embolus	0.8	84	57.4
177	Pulmonary embolus	7	97.1	81.5

Includes both type II (partial deficiency) and type III (complete deficiency) cells.

Diagnosed in the 1960s.