Table 2.

Improved expression and efficacy of the mLARβΔγV5 vector in murine β-thalassemia


Transplant group

n

% F*

% F cells

Vector copy

Hb, g/L

% Reticulocytes

Spleen weight, mg
Mock   5   NA   NA   NA   86 ± 3   22 ± 3.4   205 ± 21  
d432βΔγm  5   8.4 ± 2   31 ± 5   2.0 ± 0.3   103 ± 3§  17.3 ± 1.0  159 ± 7 
mLARβΔγV5   6   22 ± 4  71 ± 10  1.3 ± 0.3**  112 ± 3§††  6.4 ± 0.7§  115 ± 8§ 
Normal control
 
5
 
NA
 
NA
 
NA
 
122 ± 02§
 
4.0 ± 0.3§
 
ND
 

Transplant group

n

% F*

% F cells

Vector copy

Hb, g/L

% Reticulocytes

Spleen weight, mg
Mock   5   NA   NA   NA   86 ± 3   22 ± 3.4   205 ± 21  
d432βΔγm  5   8.4 ± 2   31 ± 5   2.0 ± 0.3   103 ± 3§  17.3 ± 1.0  159 ± 7 
mLARβΔγV5   6   22 ± 4  71 ± 10  1.3 ± 0.3**  112 ± 3§††  6.4 ± 0.7§  115 ± 8§ 
Normal control
 
5
 
NA
 
NA
 
NA
 
122 ± 02§
 
4.0 ± 0.3§
 
ND
 

Values represent the mean and SEM.

Hb indicates hemoglobin concentration; NA, not applicable; and ND, not done.

*

Amount of mα2, hγ2 present in the peripheral blood as a percentage of the total Hb.

Percentage of red cells staining for γ-globin expression as determined by FACS analysis.

Average vector copy number in PB leukocytes as determined by semiquantitative DNA PCR.

§

Statistically significant difference from mock group with P at < .01, one-sided.

Not statistically different from mock with P = .11, one-sided.

Statistically different from mock group with P < .05, one-sided.

Statistically significant difference from d432βΔγm group with P at least < .02, one-sided.

**

Not significantly different from d432βΔγm group with P = .098, 2-sided.

††

Statistically significant difference from d432βΔγm group with P < .03, one-sided.

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