Table 3.

Lifetime probability of cancer by attained age in patients (N = 2742) with Gaucher disease




Observed, no.

Expected, no.

RR (95% CI)
All cancer*  126   159   0.79 (0.67, 0.94)  
Multiple myeloma   10   1.7   5.9 (2.82, 10.82)  
Breast cancer   15   33.2   0.45 (0.25, 0.75)  
Prostate cancer   10   30.4   0.33 (0.16, 0.60)  
Colorectal cancer   6   15.5   0.39 (0.14, 0.84)  
Lung cancer   6   19.9   0.30 (0.11, 0.66)  
Hematologic
 
19
 
15.6
 
1.23 (0.73, 1.90)
 



Observed, no.

Expected, no.

RR (95% CI)
All cancer*  126   159   0.79 (0.67, 0.94)  
Multiple myeloma   10   1.7   5.9 (2.82, 10.82)  
Breast cancer   15   33.2   0.45 (0.25, 0.75)  
Prostate cancer   10   30.4   0.33 (0.16, 0.60)  
Colorectal cancer   6   15.5   0.39 (0.14, 0.84)  
Lung cancer   6   19.9   0.30 (0.11, 0.66)  
Hematologic
 
19
 
15.6
 
1.23 (0.73, 1.90)
 
*

Includes nonmelanoma skin cancers, ovarian cancer, renal carcinoma, bladder cancer, hepatocellular cancer, ganglioneuroma, neurosarcoma, angiosarcoma, thyroid carcinoma, pancreatic cancer, testicular rhabdomyosarcoma, and carcinoid tumor.

Includes non-Hodgkin lymphoma (5), Hodgkin disease (1), acute myeloid leukemia (AML; 3), acute lymphoblastic leukemia (ALL; 1), chronic lymphocytic leukemia (CLL; 1), Waldenstrom macroglobulinemia (1), and unspecified (7).

Close Modal

or Create an Account

Close Modal
Close Modal