Link between immunoprofiles or domain-specific anti-ADAMTS13 autoantibodies and Benhamou score, age, and cerebral involvement. (A) Benhamou score according to the 3 most prevalent immunoprofiles. The Benhamou score (<3 [1-2]; ≥3 [3-4]) was calculated based on age, cerebral involvement, and lactate dehydrogenase level.³¹ χ² test; P = .4933. (B) Age of patients according to the 3 most prevalent immunoprofiles. Kruskal-Wallis test followed by Dunn’s multiple comparisons test; P = .0333. (C) Age of patients according to the presence and absence of anti-T2-T5 autoantibodies. Mann-Whitney test, P = .0012. (D) Cerebral involvement according to the presence and absence of anti-CUB1-2 autoantibodies. Fisher’s exact test; P = .0177.