Exogenous fucose can restore fucosylation in cells of the new patient. (A) Fibroblasts derived from patient G were cultured without or with 10 mM l-fucose for 48 hours before they were analyzed for AAL binding. (B) Fibroblasts of patient G were transfected with the GFP-tagged GFTP of this patient and cultured without or with 10 mM l-fucose for 48 hours. Staining of GFP and golgin-97 is shown. One representative experiment of 3 is shown. Bars represent 10 μm.