Preliminary criteria for the classification of CAPS
Adapted from Asherson et al.7
*Clinical evidence of vessel occlusion confirmed by imaging techniques. Renal involvement defined by 50% rise in serum creatinine, severe systemic hypertension (> 180/100 mm Hg), and/or proteinuria (> 500 mg/24 h).
†Significant evidence of thrombosis must be present but vasculitis may coexist.
‡aPL detected on 2 or more occasions at least 12 weeks apart as per Miyakis et al.2