Cause and time of deaths occurring in patients who did not receive transplantation within the first year of treatment (n=64). The majority of patients died with or from active HLH (). The causes of death in 4 patients who did not have active HLH at death (■) were: fatal bleeding following liver biopsy (n=1, 7th week); septicemia where HLH status at death is not known (n=1, 2nd week), and cause of death not stated (n=2, 1st and 38th weeks). One patient who died with or from active HLH is not represented in the graph, since the exact death date is missing.