Fig. 2.
vWF-cleaving protease activity in plasma from 111 patients with TMA as a function of the clinical context.
vWF-cleaving protease activity was measured during an acute event in 42 idiopathic and 69 secondary forms of TMA. Patients were presenting as TTP (●) or HUS (○). The dashed line shows the lower limit of normal (50%). PAH indicates pulmonary arterial hypertension.