Typical clinical and imaging features of ECD. (A) Mass of the right atrium and of the atrioventricular sulcus (blue arrows). (B) Hypermetabolism of long bones, aorta, and right atrium in 18 fluorodeoxyglucose PET. (C) Pseudotumoral infiltration of brain (MRI, T1 weighted image with gadolinium), yellow arrow. (D) Typical xanthelasma palpebrarum