Figure 1.
Patients included in the study. PFD, platelet function defect; CFD, coagulation factor deficiency; *Definite PFD in at least 2 different occasions, defined by abnormalities in LTA with 2 or more agonists. †Possible PFD defined by abnormal LTA curves upon stimulation with 1 or more agonists or when platelet function was investigated at only 1 occasion; includes 2 patients with additional mild FXI deficiency (≤60%). ‡CFDs include FVIII activity ≤50% (n = 14; 60.9%); FIX activity ≤50% (n = 5; 21.7%), FXI activity ≤60% (n = 3; 13.0%), and FXIII activity ≤10% (n = 1; 4.3%).