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Journal Articles

Assessment of the Plasmic Score Utility for Classification of Pediatric Thrombotic Microangiopathies

Grace E Linder, MD, Steven Richard Sloan, MD PhD, Pavan Bendapudi, MD, Robert Makar, MD PhD

Blood (2019) 134 (Supplement_1): 1075.

https://doi.org/10.1182/blood-2019-130608

Published: 2019

Journal Articles

Description of the First Cases with ADAMTS13 Mutations in Hungary

Marienn Réti, MD, György Sinkovits, MD, Orsolya Cseprekál, MD PhD, Dorottya Csuka, PhD, Ágnes Szilágyi, PhD, Zita Farkas, MD, Zsolt Klucsik, MD, Attila Szederjesi, MSC, László Wágner, MD Prof, György Reusz, MD Prof, Johanna A. Kremer Hovinga, MD Prof, János Rigó, MD Prof, Tamas Masszi, MD Prof., Zoltan Prohászka, MD Prof

Blood (2018) 132 (Supplement 1): 5003.

https://doi.org/10.1182/blood-2018-99-118327

Published: 2018

Journal Articles

Pharmacodynamic Profile of a Recombinant ADAMTS13 (BAX930) in Hereditary Thrombotic Thrombocytopenic Purpura (Upshaw-Schulman Syndrome (USS))

Marie Scully, Paul Knoebl, MD, Karim Kentouche, Lawrence Rice, MD, Jerzy Windyga, MD, Reinhard Schneppenheim, Johanna A Kremer Hovinga, MD PhD, Michiko Kajiwara, Caterina Maggiore, Jennifer Doralt, Leah Martell, Bruce M. Ewenstein

Blood (2016) 128 (22): 135.

https://doi.org/10.1182/blood.V128.22.135.135

Published: 2016

Journal Articles

Functional Analysis Of TTP-Associated ADAMTS13 Mutants Under Shear Flow

Maria A. Brehm, PhD, Emma Kraus, B.Sc., Tobias Obser, Reinhard Schneppenheim, MD, PhD

Blood (2013) 122 (21): 1094.

https://doi.org/10.1182/blood.V122.21.1094.1094

Published: 2013

Journal Articles

Unexpected High Frequency of Upshaw-Schulman Syndrome in Norway

Anne-Sophie von Krogh, MD, Anders Waage, MD, PhD, Johanna A. Kremer Hovinga Strebel, MD, Petter Quist-Paulsen, MD, PhD

Blood (2012) 120 (21): 3315.

https://doi.org/10.1182/blood.V120.21.3315.3315

Published: 2012

Journal Articles

International Registry for Patients with Hereditary Thrombotic Thrombocytopenic Purpura (TTP) – Upshaw-Schulman Syndrome

Magnus Mansouri Taleghani, Yoshihiro Fujimura, MD, PhD, James N. George, MD, Ingrid Hrachovinova, PhD, Paul Knoebl, MD, Bernhard Lämmle, MD, Petter Quist-Paulsen, MD, PhD, Reinhard Schneppenheim, MD, PhD, Johanna A. Kremer Hovinga Strebel, MD

Blood (2012) 120 (21): 4654.

https://doi.org/10.1182/blood.V120.21.4654.4654

Published: 2012

Journal Articles

Unexpected frequency of Upshaw-Schulman syndrome in pregnancy-onset thrombotic thrombocytopenic purpura

Marie Moatti-Cohen, Céline Garrec, Martine Wolf, Pierre Boisseau, Lionel Galicier, Elie Azoulay, Alain Stepanian, Yahsou Delmas, Eric Rondeau, Stéphane Bezieau, Paul Coppo, Agnès Veyradier

Blood (2012) 119 (24): 5888–5897.

https://doi.org/10.1182/blood-2012-02-408914

Published: 2012

Includes: Supplemental data

Journal Articles

A Large-Pore IEF Gel Electrophoresis Separates the Complex in Both of ADAMTS13 Bound to VWF and to the IgG Autoantibodies From the Unbound in Plasma Milieu

Masanori Matsumoto, MD, PhD, Ayami Isonishi, BS, Yuji Hori, BS, Masaki Hayakawa, MD, Kenji Soejima, PhD, Yoshihiro Fujimura, MD, PhD

Blood (2011) 118 (21): 1160.

https://doi.org/10.1182/blood.V118.21.1160.1160

Published: 2011

Journal Articles

Correction of ADAMTS13 Deficiency by AAV-Mediated Gene Transfer of a C-Terminal Truncated ADAMTS13 Variant In a Murine Model

Sheng-Yu Jin, M.D., Ph.D., Juan (Jenny) Xiao, M.D., Ph.D., J. Fraser Wright, Ph.D., X. Long Zheng, M.D., Ph.D.

Blood (2010) 116 (21): 251.

https://doi.org/10.1182/blood.V116.21.251.251

Published: 2010

Journal Articles

Species-Dependent Variability of ADAMTS-13 Mediated Proteolysis of Human Recombinant von Willebrand Factor.

Katalin Varadi, PhD, Hanspeter Rottensteiner, PhD, Peter L. Turecek, PhD, Jutta Schreiner, Herbert Gritsch, Bernhard Baumgartner, DVM, Eva-Maria Muchitsch, DVM, Hartmut Ehrlich, MD, Hans Peter Schwarz, MD

Blood (2007) 110 (11): 2139.

https://doi.org/10.1182/blood.V110.11.2139.2139

Published: 2007

Journal Articles

Natural History of 33 Patients with Upshaw-Schulman Syndrome Has Revealed That All the Gravida Develop Thrombocytopenia, Often Followed by Thrombotic Microangiopathy with Stillbirth.

Blood (2007) 110 (11): 3211.

https://doi.org/10.1182/blood.V110.11.3211.3211

Published: 2007

Journal Articles

Upshaw-Schulman Syndrome Revealed by Pregnancy.

Masako Seike, MD, Teruhiko Kozuka, MD, Koichi Kokame, MD, Toshiyuki Miyata, MD, Tomomi Matsuyama, MD, Masanori Matsumoto, MD, Yoshihiro Fujimura, MD, Masamichi Hara, MD

Blood (2006) 108 (11): 3951.

https://doi.org/10.1182/blood.V108.11.3951.3951

Published: 2006

Journal Articles

Monoclonal Antibodies to a VWF-A2 Decapeptide with the C-Terminal Residue Tyr1605, Generated by ADAMTS13 Cleavage, Develop a Highly Sensitive ELISA for Its Activity and Characterize Upshaw-Schulman Syndrome.

Seiji Kato, PhD, Masanori Matsumoto, MD, Tomomi Matsuyama, MD, Hisahide Hiura, PhD, Yoshihiro Fujimura, MD

Blood (2005) 106 (11): 2643.

https://doi.org/10.1182/blood.V106.11.2643.2643

Published: 2005

Journal Articles

Upshaw-Schulman Syndrome: A Masqueraded Thrombocytopenia during Pregnancy.

Tomomi Matsuyama, Masanori Matsumoto, Seiji Kato, Nobu Akiyama, Junji Tomiyama, Kazuhiko Natori, Yasunobu Kuraishi, Yutaka Imamura, Nobumasa Inoue, Koichi Kokame, Toshiyuki Miyata, Yoshihiro Fujimura

Blood (2005) 106 (11): 2644.

https://doi.org/10.1182/blood.V106.11.2644.2644

Published: 2005

Journal Articles

Heightened Proteolysis of Plasma ADAMTS13 Antigen in Patients with Thrombotic Thrombocytopenic Purpura.

Hideo Yagi, MD, Masanori Matsumoto, MD, Taka-aki Iwamoto, Hiromichi Ishizachi, MD, Hitomi Nishimura, Ayami Isonishi, Kenji Soejima, PhD, Tomohiro Nakagaki, PhD, Toshio Mori, PhD, Yoshihiro Fujimura, MD

Blood (2004) 104 (11): 3946.

https://doi.org/10.1182/blood.V104.11.3946.3946

Published: 2004

Journal Articles

Molecular characterization of ADAMTS13 gene mutations in Japanese patients with Upshaw-Schulman syndrome

Masanori Matsumoto, Koichi Kokame, Kenji Soejima, Masayoshi Miura, Syuhei Hayashi, Yasuhiko Fujii, Asayuki Iwai, Etsuro Ito, Yoichiro Tsuji, Mayuko Takeda-Shitaka, Mitsuo Iwadate, Hideaki Umeyama, Hideo Yagi, Hiromichi Ishizashi, Fumiaki Banno, Tomohiro Nakagaki, Toshiyuki Miyata, Yoshihiro Fujimura

Blood (2004) 103 (4): 1305–1310.

https://doi.org/10.1182/blood-2003-06-1796

Published: 2004

Journal Articles

Thrombopoietin in Upshaw-Schulman Syndrome

Masayoshi Miura, Shoichi Koizumi, Hiroshi Miyazaki

Blood (1997) 89 (12): 4663.

https://doi.org/10.1182/blood.V89.12.4663

Published: 1997

NARROW

Assessment of the Plasmic Score Utility for Classification of Pediatric Thrombotic Microangiopathies

Description of the First Cases with ADAMTS13 Mutations in Hungary

Pharmacodynamic Profile of a Recombinant ADAMTS13 (BAX930) in Hereditary Thrombotic Thrombocytopenic Purpura (Upshaw-Schulman Syndrome (USS))

Functional Analysis Of TTP-Associated ADAMTS13 Mutants Under Shear Flow

Unexpected High Frequency of Upshaw-Schulman Syndrome in Norway

International Registry for Patients with Hereditary Thrombotic Thrombocytopenic Purpura (TTP) – Upshaw-Schulman Syndrome

Unexpected frequency of Upshaw-Schulman syndrome in pregnancy-onset thrombotic thrombocytopenic purpura

A Large-Pore IEF Gel Electrophoresis Separates the Complex in Both of ADAMTS13 Bound to VWF and to the IgG Autoantibodies From the Unbound in Plasma Milieu

Correction of ADAMTS13 Deficiency by AAV-Mediated Gene Transfer of a C-Terminal Truncated ADAMTS13 Variant In a Murine Model

Species-Dependent Variability of ADAMTS-13 Mediated Proteolysis of Human Recombinant von Willebrand Factor.

Natural History of 33 Patients with Upshaw-Schulman Syndrome Has Revealed That All the Gravida Develop Thrombocytopenia, Often Followed by Thrombotic Microangiopathy with Stillbirth.

Upshaw-Schulman Syndrome Revealed by Pregnancy.

Monoclonal Antibodies to a VWF-A2 Decapeptide with the C-Terminal Residue Tyr1605, Generated by ADAMTS13 Cleavage, Develop a Highly Sensitive ELISA for Its Activity and Characterize Upshaw-Schulman Syndrome.

Upshaw-Schulman Syndrome: A Masqueraded Thrombocytopenia during Pregnancy.

Heightened Proteolysis of Plasma ADAMTS13 Antigen in Patients with Thrombotic Thrombocytopenic Purpura.

Molecular characterization of ADAMTS13 gene mutations in Japanese patients with Upshaw-Schulman syndrome

Thrombopoietin in Upshaw-Schulman Syndrome

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